Functional asplenia in hemoglobin SC disease
نویسندگان
چکیده
منابع مشابه
Functional asplenia in hemoglobin SE disease.
The incidence of functional asplenia in sickle-hemoglobin C (SC) disease has not been defined, and the use of prophylactic penicillin to prevent life-threatening septicemia in this disorder is controversial. The percentage of red blood cells with pits (pit count) is a reliable assay of splenic function in other disorders but has not been validated in hemoglobin SC disease. To address these issu...
متن کاملDyspnea with hemoglobin SC disease.
BUMC PROCEEDINGS 2002;15:86–90 CASE PRESENTATION LINDA S. BANG, MD: A 41-year-old African American woman with sickle cell disease presented to the Baylor University Medical Center emergency department with dyspnea and dry cough for 3 weeks and back, leg, and chest pain for 2 to 3 days. The hemoglobin SC disease had been first diagnosed during pregnancy. Pleural tuberculosis with a left-sided ef...
متن کاملElevated hypercoagulability markers in hemoglobin SC disease.
Hemoglobin SC disease is a very prevalent hemoglobinopathy; however, very little is known about this condition specifically. There appears to be an increased risk of thromboembolic events in hemoglobin SC disease, but studies evaluating the hemostatic alterations are lacking. We describe the findings of a cross-sectional observational study evaluating coagulation activation markers in adult pat...
متن کاملHemoglobin SC disease and proliferative retinopathy.
Retinopathy is one of the clinical signs of hemoglobin SC disease.1 It is often misunderstood and diagnosed late because it is initially asymptomatic due to its preferential localization in the periphery of the retina.2,3 A 25-year-old man from the Ivory Coast was admitted because of an abdominal pain crisis. The patient, who had sickle cell trait, had mild scleral jaundice and pronounced splen...
متن کاملDual Case Report of Hemoglobin SC Disease in Pregnancy
Heterozygous hemoglobin sickle cell disease (HbSC) is the second most frequent hemoglobinopathy behind SCA [1]. Individuals with HbSC are heterozygous having received the βC-gene for hemoglobin C from one parent and the βS-gene for hemoglobin S from the other parent [2,3]. HbSC red cells contain equal levels of HbS and HbC. The blood smears of individuals with HbSC contain primarily Target cell...
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ژورنال
عنوان ژورنال: Blood
سال: 1995
ISSN: 0006-4971,1528-0020
DOI: 10.1182/blood.v85.8.2238.bloodjournal8582238